Collagen VII maintains proteostasis in dermal fibroblasts by scaffolding TANGO1 cargo - Qingqing Cao; Grace Tartaglia; Michael Alexander; Pyung Hung Park; Shiv Poojan; Mehdi Farshchian; FUENTES BUSTOS, MARIA IGNACIA; Mei Chen; John A. McGrath; PALISSON ETCHARREN, FRANCIS; Julio Salas-Alanis; Andrew P. South (My University, 2022)
Keywords: and tgfβ signaling; collagen vii; er stress; recessive dystrophic epidermolysis bullosa; tango1; thrombospondin; 4 [4 (1,3 benzodioxol 5 yl) 5 (2 pyridinyl) 1h imidazol 2 yl]benzamide; coat protein; coat protein complex ii; collagen type 1; collagen type 12; collagen type 7; endoplasmic reticulum chaperone bip; hydroxyproline; membrane protein; protein glutamine gamma glutamyltransferase 2; sec31 protein; smad3 protein; small interfering rna; thapsigargin; thrombospondin; thrombospondin 1; transforming growth factor beta; transport and golgi organization 1 protein; tunicamycin; unclassified drug; adult; article; cell isolation; cell stress; confocal microscopy; disease severity; endoplasmic reticulum stress; epidermolysis bullosa dystrophica; extracellular matrix; fibroblast; human; human cell; immunoblotting; immunoprecipitation; protein expression; protein homeostasis; protein secretion; tgf beta signaling; wild type