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  4. Refractory systemic juvenile idiopathic arthritis successfully treated with rapamycin
Details

Refractory systemic juvenile idiopathic arthritis successfully treated with rapamycin

Journal
Rheumatology
ISSN
1462-0324
1462-0332
Date Issued
2021
Author(s)
Sara Concha
Emma Rey-Jurado
Facultad de Medicina Clínica Alemana Universidad del Desarrollo  
M Cecilia Poli
Facultad de Medicina Clínica Alemana Universidad del Desarrollo  
Rodrigo Hoyos-Bachiloglu
Arturo Borzutzky
Type
Resource Types::text::journal::journal article
Scopus ID
2-s2.0-85110499096
WoS ID
WOS:000672804500011
DOI
10.1093/rheumatology/keab114
URL
https://investigadores.udd.cl/handle/123456789/6447
Project(s)
Deciphering the mechanisms of disease and therapeutic targets for proteasome maturation protein (pomp) related autoinflammation and immune dysregulation  
Subjects
antibodies, monoclonal, humanized

; 

antirheumatic agents

; 

arthritis, juvenile

; 

child

; 

cyclosporine

; 

female

; 

glucocorticoids

; 

humans

; 

immunosuppressive agents

; 

methotrexate

; 

nf-kappab inhibitor alpha

; 

piperidines

; 

pyrimidines

; 

severity of illness index

; 

sirolimus

; 

treatment failure

; 

tumor necrosis factor inhibitors

; 

bisphosphonic acid derivative

; 

c reactive protein

; 

canakinumab

; 

cyclosporine

; 

ferritin

; 

immunoglobulin enhancer binding protein

; 

infliximab

; 

methotrexate

; 

methylprednisolone

; 

prednisone

; 

rapamycin

; 

tocilizumab

; 

tofacitinib

; 

antirheumatic agent

; 

canakinumab

; 

cyclosporine

; 

glucocorticoid

; 

i kappa b kinase alpha

; 

immunosuppressive agent

; 

methotrexate

; 

monoclonal antibody

; 

nfkbia protein, human

; 

piperidine derivative

; 

pyrimidine derivative

; 

rapamycin

; 

tocilizumab

; 

tofacitinib

; 

tumor necrosis factor inhibitor

; 

abdominal pain

; 

blood cell count

; 

case report

; 

child

; 

clinical article

; 

clinical feature

; 

cushing syndrome

; 

disease activity

; 

disease exacerbation

; 

disease severity

; 

drug dose reduction

; 

drug megadose

; 

drug substitution

; 

drug withdrawal

; 

erythrocyte sedimentation rate

; 

female

; 

fever

; 

follow up

; 

genetic variability

; 

heterozygosity

; 

human

; 

hypertension

; 

immune deficiency

; 

laboratory test

; 

letter

; 

macrophage activation syndrome

; 

monotherapy

; 

obesity

; 

osteoporosis

; 

polyarthritis

; 

positron emission tomography-computed tomography

; 

protein blood level

; 

relapse

; 

remission

; 

school child

; 

side effect

; 

spine fracture

; 

systemic juvenile idiopathic arthritis

; 

genetics

; 

juvenile rheumatoid arthritis

; 

severity of illness index

; 

treatment failure
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