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  4. Case Report: Tocilizumab as time-limited induction therapy enabling steroid withdrawal and conventional maintenance in refractory cutaneous polyarteritis nodosa
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Case Report: Tocilizumab as time-limited induction therapy enabling steroid withdrawal and conventional maintenance in refractory cutaneous polyarteritis nodosa

Journal
Frontiers in Medicine
ISSN
2296-858X
Date Issued
2026-05-29
Author(s)
Joo Hu, Ka Wei Katty
Facultad de Medicina Clínica Alemana Universidad del Desarrollo  
Jaederlund, Fiona
Facultad de Medicina Clínica Alemana Universidad del Desarrollo  
Lohse, Fernando
Facultad de Medicina Clínica Alemana Universidad del Desarrollo  
Karsulovic, Claudio
Facultad de Medicina Clínica Alemana Universidad del Desarrollo  
HOJMAN CANO, LIA PAULA  
Facultad de Medicina Clínica Alemana Universidad del Desarrollo  
Type
Article
DOI
10.3389/fmed.2026.1861077
URL
https://investigadores.udd.cl/handle/123456789/12620
Abstract
Background


Cutaneous polyarteritis nodosa (CPAN) is a chronic, relapsing vasculitis frequently associated with glucocorticoid dependence and the absence of standardized treatment algorithms. Therapeutic decisions are largely empirical and management of refractory disease remains challenging.





Case presentation


We report a patient with refractory CPAN and persistent steroid dependence despite corticosteroids and conventional immunosuppressive therapies. A deliberately planned, time-limited induction strategy with tocilizumab (TCZ) was implemented to achieve rapid disease control and enable steroid withdrawal, followed by maintenance with mycophenolate mofetil (MMF).





Results


TCZ led to rapid clinical remission after two infusions, allowing progressive steroid tapering and discontinuation. After six doses, TCZ was stopped and MMF was introduced as maintenance therapy. The patient remains lesion-free at the time of manuscript submission.





Conclusion


A time-limited IL-6 blockade strategy may allow rapid steroid withdrawal and facilitate transition to conventional maintenance in refractory CPAN. This approach may reduce cumulative exposure to both glucocorticoids and biologic agents.
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